英文名称 Anti-GLA Polyclonal Antibody 靶标 GLA 别名 GALA;Alpha-galactosidase A;Alpha-D-galactosidase A;Alpha-D-galactoside galactohydrolase;Galactosylgalactosylglucosylceramidase GLA;Melibiase; Agalsidase;AGAL_HUMAN;Agalsidase alfa;Alpha D galactosidase A;Alpha gal A; 宿主 Rabbit 稀释比例 IHC 1:50-200. Gene ID 2717 保存 Store at -20°C. Avoid freeze / thaw cycles. Swiss Prot P06280 蛋白分子量 79kDa 储存液 Buffer: PBS with 0.03% Proclin300, 50% glycerol, pH7.3. 亚细胞定位 Cytoplasm 免疫原 Recombinant protein of human GLA 亚型 IgG 纯化方法 Affinity purification 背景资料 This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. Public Immunogen Range 1-350aa 克隆类型 Polyclonal Antibody 交叉反应 Human;Mouse 应用 IHC 规格 50ul 100ul 使用前请离心。如有问题请及时联系我们。